Your shopping cart is empty!
Anti-HADHA Rabbit pAb (100 μl)
| Reactivity: | M,R |
| Applications: | WB |
| Host Species: | Rabbit |
| Clonality: | Polyclonal |
| Full Name: | HADHA rabbit polyclonal antibody |
Gene Name: | Trifunctional enzyme subunit alpha, mitochondrial |
Synonyms: | Monolysocardiolipin acyltransferase, TP-alpha, HADHA |
Immunogen: | KLH conjugated Synthetic peptide corresponding to Mouse HADHA |
Isotype: | IgG |
Purity: | Affinity purification |
Predicted MW. | 83 kDa |
Observed MW. | 74 kDa |
Uniprot ID: | Q8BMS1, Q64428 |
Product Usage Information
Applications | Species | Dilution | Positive Sample |
WB | Mouse, Rat | 1: 500-1: 1000 | heart, liver, kidney |
Background
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency.
Images
|
|
Western blot analysis of HADHA (GB111284) at dilution of 1: 500 |
Storage
| Storage | Store at -20°C for one year. Avoid repeated freeze/ thaw cycles. |
| Storage Buffer | PBS with 0.02% sodium azide, 100 μg/ml BSA and 50% glycerol. |
