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Anti-Fumarylacetoacetate hydrolase/FAA Rabbit pAb (100 μl)
| Reactivity: | M,R |
| Applications: | WB |
| Host Species: | Rabbit |
| Clonality: | Polyclonal |
| Full Name: | Fumarylacetoacetate hydrolase/FAA rabbit polyclonal antibody |
Gene Name: | Fumarylacetoacetase |
Synonyms: | Beta diketonase, FAA, FAH, Fumarylacetoacetate hydrolase |
Immunogen: | KLH conjugated Synthetic peptide corresponding to Mouse FAA |
Isotype: | IgG |
Purity: | Affinity purification |
Predicted MW. | 46 kDa |
Observed MW. | 40 kDa |
Uniprot ID: | P35505 |
Product Usage Information
Applications | Species | Dilution | Positive Sample |
WB | Mouse, Rat | 1: 1000-1: 3000 | liver, kidney |
Background
FAH is also named as FAA(fumarylacetoacetase), the last enzyme in tyrosine degradation, functionally important in the liver and kidney(PMID:8473520). FAH is a metabolic enzyme catalyzing the last step of tyrosine and phenylalanine catabolism: the hydrolysis of fumarylacetoacetate into acetoacetate and fumarate. In humans, deficiency of this activity is associated with the metabolic disease hereditary tyrosinaemia type I, which is also known as hepatorenal tyrosinaemia.
Images
| Western blot analysis of FAH (GB114085) at dilution of 1: 1000 |
Storage
| Storage | Store at -20°C for one year. Avoid repeated freeze/thaw cycles. |
| Storage Buffer | PBS with 0.02%sodium azide,100 μg/ml BSA and 50% glycerol. |
