Your shopping cart is empty!
Anti-HADHA Rabbit pAb (100 μl)
| Reactivity: | H,M,R |
| Applications: | WB |
| Host Species: | Rabbit |
| Clonality: | Polyclonal |
| Full Name: | HADHA rabbit polyclonal antibody |
Gene Name: | Trifunctional enzyme subunit alpha, mitochondrial |
Synonyms: | Monolysocardiolipin acyltransferase, TP-alpha, Long-chain enoyl-CoA hydratase, GBP, HADHA, 3 oxoacyl CoA thiolase, MTPA |
Immunogen: | Recombinant protein corresponding to Mouse HADHA |
Isotype: | IgG |
Purity: | Affinity purification |
Predicted MW. | 83 kDa |
Observed MW. | 74 kDa |
Uniprot ID: | P40939, Q8BMS1, Q64428 |
Product Usage Information
Applications | Species | Dilution | Positive tissue |
WB | Human, Mouse, Rat | 1: 500-1: 1000 | stomach, pancreas |
Background
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
Images
| Western blot analysis of HADHA (GB112034) at dilution of 1: 500 |
Storage
| Storage | Store at -20°C for one year. Avoid repeated freeze/thaw cycles. |
| Storage Buffer | PBS with 0.02%sodium azide,100 μg/ml BSA and 50% glycerol. |
